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Suppression of Organelle Defects in Human Disease

CORDIS provides links to public deliverables and publications of HORIZON projects.

Links to deliverables and publications from FP7 projects, as well as links to some specific result types such as dataset and software, are dynamically retrieved from OpenAIRE .

Publications

DNA Structure-Specific Cleavage of DNA-Protein Crosslinks by the SPRTN Protease

Author(s): Hannah K. Reinking, Hyun-Seo Kang, Maximilian J. Götz, Hao-Yi Li, Anja Kieser, Shubo Zhao, Aleida C. Acampora, Pedro Weickert, Evelyn Fessler, Lucas T. Jae, Michael Sattler, Julian Stingele
Published in: Molecular Cell, Issue 80/1, 2020, Page(s) 102-113.e6, ISSN 1097-2765
Publisher: Cell Press
DOI: 10.1016/j.molcel.2020.08.003

DELE1 tracks perturbed protein import and processing in human mitochondria

Author(s): Evelyn Fessler, Luisa Krumwiede & Lucas T. Jae
Published in: Nature Communications, Issue 20411723, 2022, ISSN 2041-1723
Publisher: Nature Publishing Group
DOI: 10.1038/s41467-022-29479-y

Sensing, signaling and surviving mitochondrial stress

Author(s): Eva-Maria Eckl, Olga Ziegemann, Luisa Krumwiede, Evelyn Fessler, Lucas T. Jae
Published in: Cellular and Molecular Life Sciences, Issue 78/16, 2021, Page(s) 5925-5951, ISSN 1420-682X
Publisher: Birkhauser Verlag
DOI: 10.1007/s00018-021-03887-7

OMA1 mediates local and global stress responses against protein misfolding in CHCHD10 mitochondrial myopathy

Author(s): Mario K. Shammas, Xiaoping Huang, Beverly P. Wu, Evelyn Fessler, Insung Y. Song, Nicholas P. Randolph, Yan Li, Christopher K.E. Bleck, Danielle A. Springer, Carl Fratter, Ines A. Barbosa, Andrew F. Powers, Pedro M. Quirós, Carlos Lopez-Otin, Lucas T. Jae, Joanna Poulton, and Derek P. Narendra
Published in: The Journal of Clinical Investigation, Issue 00219738, 2022, ISSN 0021-9738
Publisher: American Society for Clinical Investigation
DOI: 10.1172/jci157504

A pathway coordinated by DELE1 relays mitochondrial stress to the cytosol

Author(s): Evelyn Fessler, Eva-Maria Eckl, Sabine Schmitt, Igor Alves Mancilla, Matthias F. Meyer-Bender, Monika Hanf, Julia Philippou-Massier, Stefan Krebs, Hans Zischka, Lucas T. Jae
Published in: Nature, Issue 579/7799, 2020, Page(s) 433-437, ISSN 0028-0836
Publisher: Nature Publishing Group
DOI: 10.1038/s41586-020-2076-4

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