CLUH maintains functional mitochondria and translation in motoneuronal axons and prevents peripheral neuropathy
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Autores:
Marta Zaninello, Tim Schlegel, Hendrik Nolte, Mujeeb Pirzada, Elisa Savino, Esther Barth, Ines Klein, Hauke Wüstenberg, Tesmin Uddin, Lisa Wolff, Brunhilde Wirth, Helmar C. Lehmann, Jean-Michel Cioni, Thomas Langer, Elena I. Rugarli
Publicado en:
Science Advances, Edición 10, 2024, ISSN 2375-2548
Editor:
American Association for the Advancement of Science (AAAS)
DOI:
10.1126/sciadv.adn2050
Neuronal models of TDP-43 proteinopathy display reduced axonal translation, increased oxidative stress, and defective exocytosis
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Autores:
Alessandra Pisciottani, Laura Croci, Fabio Lauria, Chiara Marullo, Elisa Savino, Alessandro Ambrosi, Paola Podini, Marta Marchioretto, Filippo Casoni, Ottavio Cremona, Stefano Taverna, Angelo Quattrini, Jean-Michel Cioni, Gabriella Viero, Franca Codazzi, G. Giacomo Consalez
Publicado en:
Frontiers in Cellular Neuroscience, Edición 17, 2023, ISSN 1662-5102
Editor:
Frontiers Research Foundation
DOI:
10.3389/fncel.2023.1253543